Catalog No.
RHC92201
Species reactivity
Human
Host species
Rabbit
Isotype
IgG
Clonality
Monoclonal
Tested applications
IF: 1:50-1:200, IHC: 1:50-1:100, WB: 1:500-1:1000
Target
COL6A1, Collagen alpha-1(VI) chain
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Accession
P12109
Applications
IF, IHC, WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4, 0.05% BSA, 50% Glycerol, 0.05% Sodium azide.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze thaw cycles. Store at 4 ℃ for frequent use. Store at -20 ℃ for twelve months from the date of receipt.
Clone ID
R1N58
The UCMD-Causing COL6A1 (c.930 + 189C > T) Intron Mutation Leads to the Secretion and Aggregation of Single Mutated Collagen VI α1 Chains., PMID:40225172
Involvement of muscle satellite cell dysfunction in neuromuscular disorders: Expanding the portfolio of satellite cell-opathies., PMID:35302338
Gapmer Antisense Oligonucleotides to Selectively Suppress the Mutant Allele in COL6A Genes in Dominant Ullrich Congenital Muscular Dystrophy., PMID:32865794
Localization, fate and interactions of Emilin-1 in human skin., PMID:30843221
The circadian regulator Bmal1 in joint mesenchymal cells regulates both joint development and inflammatory arthritis., PMID:30612576
Identification of a common epitope in the sequences of COL4A1 and COL6A1 recognized by monoclonal antibody #141., PMID:30321347
Type VI collagen α1 chain polypeptide in non-triple helical form is an alternative gene product of COL6A1., PMID:29659864
Authentication of collagen VI antibodies., PMID:28755659
RANKL expressed on synovial fibroblasts is primarily responsible for bone erosions during joint inflammation., PMID:26025971
Lack of Collagen VI Promotes Wound-Induced Hair Growth., PMID:25989472
Accessibilome of human glioblastoma: collagen-VI-alpha-1 is a new target and a marker of poor outcome., PMID:25325876
Influence of ranibizumab treatment on the extracellular matrix in patients with neovascular age-related macular degeneration., PMID:24866589
Collagen VI regulates satellite cell self-renewal and muscle regeneration., PMID:23743995
A pilot study comparing protein expression in different segments of the normal colon and rectum and in normal colon versus adenoma in patients with Lynch syndrome., PMID:23604467
[Clinical and mutation analyses of a Chinese family with Bethlem myopathy]., PMID:23290209
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis., PMID:22226732
Expression of the collagen VI α5 and α6 chains in normal human skin and in skin of patients with collagen VI-related myopathies., PMID:20882040
Identification and characterization of novel collagen VI non-canonical splicing mutations causing Ullrich congenital muscular dystrophy., PMID:19309692
A refined diagnostic algorithm for Bethlem myopathy., PMID:18378883
The congenital muscular dystrophies: recent advances and molecular insights., PMID:17163796
Dominant and recessive COL6A1 mutations in Ullrich scleroatonic muscular dystrophy., PMID:16130093
Collagen VI deficiency affects the organization of fibronectin in the extracellular matrix of cultured fibroblasts., PMID:11691587
Collagen VI deficiency induces early onset myopathy in the mouse: an animal model for Bethlem myopathy., PMID:9817932
Morphological classification of nuchal skin in human fetuses with trisomy 21, 18, and 13 at 12-18 weeks and in a trisomy 16 mouse., PMID:9497154
For research use only. Not for human or drug use.
