Catalog No.
RHG47202
Host species
Mouse
Isotype
IgG2a, kappa
Clonality
Monoclonal
Target
BTS, Battenin, Batten disease protein, Protein CLN3, CLN3
Concentration
1 mg/ml
Endotoxin level
Please contact with the lab for this information.
Purity
>95% as determined by SDS-PAGE.
Purification
Protein A/G purified from cell culture supernatant.
Applications
IHC, WB
Form
Liquid
Storage buffer
0.01M PBS, pH 7.4.
Stability and Storage
Use a manual defrost freezer and avoid repeated freeze-thaw cycles. Store at 4°C short term (1-2 weeks). Store at -20°C 12 months. Store at -80°C long term.
Clone ID
N380/95
Fluorescence Correlation Spectroscopy as a Versatile Method to Define Aptamer-Protein Interactions with Single-Molecule Sensitivity., PMID:38124657
Clinical and molecular characterization of non-syndromic retinal dystrophy due to c.175G>A mutation in ceroid lipofuscinosis neuronal 3 (CLN3)., PMID:30446867
Secretion and function of Cln5 during the early stages of Dictyostelium development., PMID:30048658
Lack of specificity of antibodies raised against CLN3, the lysosomal/endosomal transmembrane protein mutated in juvenile Batten disease., PMID:29089465
Pharmacological Effects on Ceroid Lipofuscin and Neuronal Structure in Cln3 ∆ex7/8 Mouse Brain Cultures., PMID:28812237
Aptamers Binding to c-Met Inhibiting Tumor Cell Migration., PMID:26658271
FRET-assisted determination of CLN3 membrane topology., PMID:25051496
Osmotic stress changes the expression and subcellular localization of the Batten disease protein CLN3., PMID:23840424
Immunosuppression alters disease severity in juvenile Batten disease mice., PMID:20937531
Identification of alpha-fetoprotein as an autoantigen in juvenile Batten disease., PMID:17931875
IgG entry and deposition are components of the neuroimmune response in Batten disease., PMID:17070688
Distinct patterns of serum immunoreactivity as evidence for multiple brain-directed autoantibodies in juvenile neuronal ceroid lipofuscinosis., PMID:16972881
Two novel CLN5 mutations in a Portuguese patient with vLINCL: insights into molecular mechanisms of CLN5 deficiency., PMID:16814585
Defective lysosomal arginine transport in juvenile Batten disease., PMID:16251196
Autoimmunity to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease., PMID:15728308
Glutamic acid decarboxylase autoimmunity in Batten disease and other disorders., PMID:15596740
Interconnections of CLN3, Hook1 and Rab proteins link Batten disease to defects in the endocytic pathway., PMID:15471887
CLN3L, a novel protein related to the Batten disease protein, is overexpressed in Cln3-/- mice and in Batten disease., PMID:15240430
Recruitment of Cdc28 by Whi3 restricts nuclear accumulation of the G1 cyclin-Cdk complex to late G1., PMID:14685274
Intracellular trafficking of CLN3, the protein underlying the childhood neurodegenerative disease, Batten disease., PMID:14644441
Characterization of Cln3p, the gene product responsible for juvenile neuronal ceroid lipofuscinosis, as a lysosomal integral membrane glycoprotein., PMID:14622109
Membrane topology of CLN3, the protein underlying Batten disease., PMID:12706816
An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease., PMID:12023984
Tissue distribution of products of the mouse decay-accelerating factor (DAF) genes. Exploitation of a Daf1 knock-out mouse and site-specific monoclonal antibodies., PMID:11683962
CLN3 protein is targeted to neuronal synapses but excluded from synaptic vesicles: new clues to Batten disease., PMID:11590129
CLN-3 protein is expressed in the pancreatic somatostatin-secreting delta cells., PMID:11589017
Tripeptidyl-peptidase I in neuronal ceroid lipofuscinoses and other lysosomal storage disorders., PMID:11589013
Histopathologic and immunocytochemical analysis of the retina and ocular tissues in Batten disease., PMID:10964839
Distinct subcellular localization patterns contribute to functional specificity of the Cln2 and Cln3 cyclins of Saccharomyces cerevisiae., PMID:10611233
Splicing variants in sheep CLN3, the gene underlying juvenile neuronal ceroid lipofuscinosis., PMID:10356317
Defective intracellular transport of CLN3 is the molecular basis of Batten disease (JNCL)., PMID:10332042
Tissue expression and subcellular localization of CLN3, the Batten disease protein., PMID:10191116
Posttranslational modification of CLN3 protein and its possible functional implication., PMID:10191114
Intracellular trafficking of the JNCL protein CLN3., PMID:10191111
Evidence for phosphorylation of CLN3 protein associated with Batten disease., PMID:9878558
Immunochemical localization of the Batten disease (CLN3) protein in retina., PMID:9344361
A V lambda x-bearing monoclonal antibody with similar specificity and sequence to encephalitogenic T cell receptors., PMID:7517973